4426 Hawkinsin Hawkinsin is an endogenous compound with the formula C11H17NO6S and an average molecular weight of 291.32 g/mol. It exists as a solid at room temperature. Hawkinsin belongs to the amino acids, peptides, and analogues, a subclass of carboxylic acids and derivatives within the organic compounds. It is identified as (2-l-cystein-S-yl, 4-dihydroxycyclohex-5-en-1-yl)acetic acid. Patients with hawkinsinuria excrete this metabolite in their urine throughout their life, although tyrosinemia and metabolic acidosis symptoms improve in the first year of life. Hawkinsinuria and tyrosinemia type III are causally related to alterations in the structure and activity of 4-hydroxyphenylpyruvic acid dioxygenase. It is found in or released from Electrical & Electronic Equipment (Television Systems). 63224-90-8 173909 C11H17NO6S White powder. No indication of carcinogenicity to humans (not listed by IARC). This is an endogenously produced metabolite found in the human body. It is used in metabolic reactions, catabolic reactions or waste generation. Chronically high levels of hawkinsin are associated with Hawkinsinuria. 2014-08-29T06:36:15Z 2026-04-06T13:07:43Z true NC(CSC1CC(O)C=CC1(O)CC(O)=O)C(O)=O C11H17NO6S InChI=1S/C11H17NO6S/c12-7(10(16)17)5-19-8-3-6(13)1-2-11(8,18)4-9(14)15/h1-2,6-8,13,18H,3-5,12H2,(H,14,15)(H,16,17) SPXVLTDISXZSFM-UHFFFAOYSA-N 291.321 291.077657971 Endogenous Solid HMDB02354 151775 CHEM003332 NS00125392 141.08 68.53380000000001 27.82939123320438 6 7 5 1.93942479227327 9.13420766816257 -1 1 -3.19 -1.41 1.14e+01 g/l Organic compounds Organic acids and derivatives Carboxylic acids and derivatives Amino acids, peptides, and analogues 17 CED0029863 SPXVLTDISXZSFM-UHFFFAOYSA-N 40000000000000000000800000000800000000000000000000000000000000000000000000000000000008000000000004100000000000000000000000000000000000000000000000000000000000000020000000000000000000000000000000003000010008000000000000000000040000020100000000000000000010100000000008000010040000000000000020001000000000000000000000600000000800000000000001000000000000000000100000000000000000000000000000000080000000000000400008000000000000000000000000400000000000000000000000000844020040001000000400000000000000000000000000080000 500000208102860088020040010820000000140001052000003420408220004c44020011108000000000410800800000842000a4008c32010000643101a04000c41104001200040000901020006203000000058051001a3240000422400009000c3000070048020840001040d4b40000218080500105e0041118008002110002404400088cd002080c0e0204882c0008191c0832c440140200040800004040a0404300000010c00000000840016c251046c00201894108401000023008400210802000a424c00012018002000541028000080000020050000d0002000800810090100c1000000000000004010096220400300030804200260000010050400002 776t3gAAAAAQAAAAAwAAAAAAAAATAAAAEwAAAIABBwBgAAAAAQIGAGAAAAAD AQYAYAAAAAICEAAgAAAAAgYAYAAAAAMBBgBgAAAAAgIGAGAAAAADAQgAYAAA AAEBBgBoAAAAAwMBBgBoAAAAAwMBBgAgAAAABAgAYAAAAAEBBgBgAAAAAgIG ACgAAAADBAgAaAAAAAMBAQgAKAAAAAMCBgAoAAAAAwQIAGgAAAADAQEIACgA AAADAgsAAQABAgACAwADBAAEBQAFBgAGBwAGCAAICQgCCQoACgsACgwADA0A DQ4gDQ8oAgEQABARIBASKAIKBABCAQAAAAYECgkIBgUXBAAAAAAAAAAW 2026-09-19T04:01:15Z